Editorial                   65        C Angelini: MDR '95 Conference

 Reviews                  79        mtDNA defects in degenerative disorders
                                                          N Bresolin, GP Comi, CD Ausenda, M Robotti, M Colucci and G Scarlato

                                 91        Prospects for gene therapy by gene transfer in regenerating skeletal muscle
                                             R Jerkovic, R Di Lisi, V Piovan, A Picard, R Scheepers, MT Valenti, B Sehested Hansen and S Schiaffino

 Articles                   95        A severe case of Duchenne-like muscular dystrophy due to a mutation in the a-sarcoglycan (adhalin) gene
                                            M Fanin, F Martinello, D J Duggan, J R Gorospe, MP Freda, E Pegoraro, G Sorarù, ML Mostacciuolo,
                                            CP Trevisan, EP Hoffman and C Angelini

                               101        Merosin expression in muscle of western cases with Fukuyama-like congenital muscular dystrophy
                                             CP Trevisan, F Martinello, M Fanin, P Perini, E Pastorello, M Ottina, A Piazza, C Angelini,
                                             ML Mostacciuolo, A P Tormene and C Gigante

                               107        Diagnosis and therapy of myophosphorilase deficiency: experience with a group of italian patients
                                             A Martinuzzi, G Schievano, L Vergani, M Fanin, E Pegoraro, C Schi-raldi, G Vita, G Siciliano,
                                             A Toscano and C Angelini

                               115        Muscle fatigue evaluation in the follow-up of children affected by Duchenne muscular dystrophy
                                             M Knaflitz, G Balestra, C Angelini and M Cadaldini

Communications    125        Results of idebenone treatment in patients with ocular mitochondrial myopathy
                                             G Siciliano, F Sartucci, L Manca, B Rossi, C Chisari, L Bonfiglio, L Sagliocco and L Murri

                               131        Myasthenia gravis in patient with epilepsy treated with long-term cyclosporine therapy
                                             DM Bonifati and C Angelini

                               135        Riboflavin-responsive metabolic myopathy with abnormal fatty acid oxidation and defective intramitochondrial respiratory complexes
                                             L Vergani, F Collatuzzo, G Schievano and C Angelini